Ifosiwewe XII (aito Hageman) aipe

Aito ifosiwewe XII jẹ aiṣedede ti a jogun ti o ni ipa kan amuaradagba (ifosiwewe XII) ti o ni ninu didi ẹjẹ.

Nigbati o ba ta ẹjẹ, lẹsẹsẹ awọn aati yoo waye ninu ara ti o ṣe iranlọwọ fun didi ẹjẹ. Ilana yii ni a pe ni kasikasi coagulation. O jẹ awọn ọlọjẹ pataki ti a pe ni coagulation tabi awọn ifosiwewe didi. O le ni aye ti o ga julọ ti ẹjẹ pupọ ti o ba jẹ pe ọkan tabi diẹ ẹ sii ti awọn ifosiwewe wọnyi nsọnu tabi ko ṣiṣẹ bi o ti yẹ.

Ifosiwewe XII jẹ iru ifosiwewe bẹ. Aisi ifosiwewe yii ko jẹ ki o ta ẹjẹ ni aito. Ṣugbọn, ẹjẹ gba to gun ju deede lati di ninu tube idanwo kan.

Aito ifosiwewe XII jẹ aiṣedede ti a jogun.

Ko si awọn aami aisan nigbagbogbo.

Aito ifosiwewe XII ni a rii nigbagbogbo julọ nigbati a ba ṣe awọn idanwo didi fun iṣayẹwo deede.

Awọn idanwo le pẹlu:

• Ifosiwewe XII lati wiwọn iṣẹ ti ifosiwewe XII
• Akoko thromboplastin apakan (PTT) lati ṣayẹwo bi o ṣe gun to fun ẹjẹ lati di
• Ipọpọ iwadi, idanwo PTT pataki kan lati jẹrisi aipe ifosiwewe XII

Itọju jẹ igbagbogbo ko nilo.

Awọn orisun wọnyi le pese alaye diẹ sii lori aipe aipe XII:

• Foundation Foundation ti Hemophilia - www.hemophilia.org/Bleeding-Disorders/Types-of-Bleeding-Disorders/Other-Factor-Deficiencies/Factor-XII
• Orilẹ-ede Orilẹ-ede fun Awọn rudurudu Rare - rarediseases.org/rare-diseases/factor-xii-deficiency
• NIH Ile-iṣẹ Alaye Awọn Jiini ati Rare - rarediseases.info.nih.gov/diseases/6558/factor-xii-deficiency

Abajade ni a nireti lati dara laisi itọju.

Ko si awọn ilolu nigbagbogbo.

Olupese ilera ni igbagbogbo ṣe awari ipo yii nigbati o nṣiṣẹ awọn idanwo lab miiran.

Eyi jẹ rudurudu ti a jogun. Ko si ọna ti a mọ lati ṣe idiwọ rẹ.

Aito F12; Aito ifosiwewe Hageman; Hageman iwa; Aito HAF

• Awọn didi ẹjẹ

Gailani D, Wheeler AP, Neff AT. Awọn aito ifosiwewe coagulation. Ninu: Hoffman R, Benz EJ, Silberstein LE, et al, eds. Hematology: Awọn Agbekale Ipilẹ ati Iṣe. 7th ed. Philadelphia, PA: Elsevier; 2018: ori 137.

Hall JE. Hemostasis ati coagulation ẹjẹ. Ni: Hall JE, ed. Iwe Guyton ati Hall ti Ẹkọ nipa Ẹkọ Egbogi. 13th ed. Philadelphia, PA: Elsevier; 2016: ori 37.

Ragni MV. Awọn rudurudu ẹjẹ: awọn aipe ifosiwewe coagulation. Ni: Goldman L, Schafer AI, awọn eds. Oogun Goldman-Cecil. 25th ed. Philadelphia, PA: Elsevier Saunders; 2016: ori 174.