Ovalocytosis ti a jogun

Ovalocytosis ti a jogun jẹ ipo toje ti o kọja nipasẹ awọn idile (jogun). Awọn sẹẹli ẹjẹ jẹ apẹrẹ oval dipo yika. O jẹ fọọmu ti elliptocytosis ti a jogun.
Ovalocytosis jẹ akọkọ ni awọn olugbe Iwọ-oorun Guusu ila oorun Asia.
Awọn ọmọ ikoko ti o ni ovalocytosis le ni ẹjẹ ati jaundice. Awọn agbalagba nigbagbogbo kii ṣe awọn aami aisan.
Idanwo nipasẹ olupese iṣẹ ilera rẹ le ṣe afihan ọlọ.
A ṣe ayẹwo ipo yii nipasẹ wiwo apẹrẹ awọn sẹẹli ẹjẹ labẹ maikirosikopu kan. Awọn idanwo wọnyi le tun ṣee ṣe:
- Pipe ka ẹjẹ (CBC) lati ṣayẹwo fun ẹjẹ tabi iparun sẹẹli ẹjẹ pupa
- Sisọ ẹjẹ lati pinnu apẹrẹ sẹẹli
- Ipele Bilirubin (le jẹ giga)
- Ipele dehydrogenase lactate (le jẹ giga)
- Olutirasandi ti ikun (le ṣe afihan awọn okuta iyebiye)
Ni awọn iṣẹlẹ ti o nira, a le ṣe itọju arun naa nipa yiyọ ọpa (splenectomy).
Ipo naa le ni nkan ṣe pẹlu okuta okuta tabi awọn iṣoro kidinrin.
Ovalocytosis - jogun
Awọn sẹẹli ẹjẹ
Gallagher PG. Hemolytic anemias: awo ilu ẹjẹ pupa ati awọn abawọn ti iṣelọpọ. Ni: Goldman L, Schafer AI, awọn eds. Oogun Goldman-Cecil. 26th ed. Philadelphia, PA: Elsevier; 2020: ori 152.
Gallagher PG. Awọn rudurudu awọ ara ẹjẹ pupa. Ninu: Hoffman R, Benz EJ, Silberstein LE, et al, eds. Hematology: Awọn Agbekale Ipilẹ ati Iṣe. 7th ed. Philadelphia, PA: Elsevier; 2018: ori 45.
MD Merguerian, Gallagher PG. Elliptocytosis ogún, pyropoikilocytosis ti a jogun, ati awọn rudurudu ti o jọmọ. Ni: Kliegman RM, St.Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM, eds. Nelson Iwe-ẹkọ ti Pediatrics. 21st ed. Philadelphia, PA: Elsevier; 2020: ori 486.